However, with progression of hearing loss, cochlear implants are indicated. 16 – 18 Children derive benefit from conventional hearing aids and often have close to normal speech acquisition. 6 Although thought to be non-progressive, there is evidence to indicate progression of hearing loss over the years, particularly in Usher type 2A. 15 Hearing loss is congenital and infants are detected through the newborn hearing screen, however, if unavailable detection can be overlooked till the end of the first decade of life due to the high frequency configuration and degree of hearing loss. 11 The sensorineural hearing loss is typically described as sloping, mild to moderate in the low frequencies and severe to profound in the high frequencies ( Figure 1). Usher syndrome type 2 (Usher 2) is the most common form of the disorder, representing over half of all cases. Source: Adapted from the British Association of Audiovestibular Physicians (BAAP) guidelines. 13, 14 The standard approach is to offer bilateral cochlear implants to Usher 1 patients within the first 2 years of life.įlowchart for investigation and treatment of bilateral profound sensorineural hearing loss. An earlier age of implantation is correlated with improved outcome. Timely use of cochlear implants can achieve oral communication and open set speech perception. Due to the profound nature of deafness, children with Usher 1 derive limited or no benefit from hearing aids and most patients with Usher 1 would be sign language users if the hearing loss is not treated effectively. When older, they compensate for their vestibular areflexia using vision, until the onset of RP, although they often have higher accidental falls and difficulty in performing activities, which require balance, for example, riding a bicycle. Vestibular areflexia is reflected in delayed motor development and children usually do not walk independently before the age of 18 months. 11 Infants are detected through the newborn hearing screen ( Figure 2), and where not undertaken/available, the diagnosis is often suspected in infancy. It accounts for approximately 25–44% of all Usher syndrome cases. Usher syndrome type 1 (Usher 1) is the most severe subtype in which patients exhibit severe to profound bilateral congenital sensorineural hearing loss ( Figure 1), most frequently non-progressive, with vestibular areflexia. Source: Data included from previous studies. While many promising treatments are under investigation, there is no approved treatment for this disease to date. The Usher genes encode a variety of proteins that are expressed in the inner ear and retina where they perform essential functions in sensory hair cell development and function, and photoreceptor maintenance. 2, 4 Usher syndrome is both clinically and genetically heterogeneous and is divided into three distinct clinical subtypes, associated with a number of genetic loci. 2, 3 Furthermore, it has been estimated to represent 5% of all congenital deafness and 18% of all retinitis pigmentosa (RP) cases. 1, 2 It has an estimated prevalence of between 4 and 17 in 100 000 people worldwide. It is the most common cause of combined sight and hearing loss, accounting for more than half of deaf–blindness cases. Usher syndrome encompasses a group of inherited disorders characterised by dual sensory impairment of the auditory and visual systems, with a variable presentation of vestibular dysfunction in a proportion of cases. While there is currently no available approved treatment for the RP, various therapeutic strategies are in development or in clinical trials for Usher syndrome, including gene replacement, gene editing, antisense oligonucleotides and small molecule drugs. Hearing loss is managed with hearing aids and cochlear implants, which has made a significant improvement in quality of life for patients. Genotype–phenotype correlations have been described for several of the Usher genes. Variants in these genes can also cause non-syndromic RP and deafness. To date, 10 causative genes have been identified for Usher syndrome, with MYO7A accounting for >50% of type 1 and USH2A contributing to approximately 80% of type 2 Usher syndrome. It is the most common cause of deaf–blindness worldwide with a prevalence of between 4 and 17 in 100 000. Usher syndrome has three subtypes, each being clinically and genetically heterogeneous characterised by sensorineural hearing loss and retinitis pigmentosa (RP), with or without vestibular dysfunction.
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Artillery is good for heavy damage, but is slow in reloading. Interceptors have a wide range of attack but also have mediocre firepower. Riflemen are fast, but are the weakest in terms of firepower and range. There are four different kinds of units that can be selected in the game, with each having their own strengths and weaknesses. Take note, however, that you will not be getting the full cost of units back if you decide to sell them. Coins are acquired by defeating units, and players can also earn coins by selling units that they have already deployed. Each unit has different costs, and they may also be upgraded using coins. Within the stages themselves, coins act as the currency, and these are used to purchase and deploy units. Tokens are much harder to come by than stars, but these, along with stars, can also be acquired in a variety of ways.Įxtra stars and tokens can be purchased in exchange of real life money, and they can also be earned as rewards by completing achievements which would require players to perform specific tasks such as destroying a hundred units and completing an entire set of missions, among others. On the other hand, tokens are considered as the premium currency, and these are used to buy arsenals. Stars are earned depending on how players perform during the many levels, and these are used to buy upgrades for units as well as to purchase slots for hero units. There are two types of currencies available within Toy Defense 2, namely stars and tokens. Players can promote units before and during the game, and they also have access to an arsenal of other weapons to help them along in their mission. Players must then place different units that will shoot at the enemies, with the purpose of not letting enemies get to your base. Toy Defense 2 is a tower defense game where wave after wave of enemies will walk down one or more predetermined paths towards the base. Proper strategy and management of resources is essential in winning the game, and only the best generals will be able to withstand the endless waves of enemies coming your way. In this title, war is a literal game, as players will be placing toy units in order to defend their base against similar toy soldiers, tanks, and other units. Vehicles from Great Britain, the U.S.A.If it is intense combat that you want, then let Toy Defense 2 take you to where the action is.Famous campaigns like the Battle of Iwo Jima and Operation Overlord.Three game modes: PvE missions, tournaments and PvP battles.They may be toy soldiers, but this no place for toying around! It’s up to you build an unstoppable army, take on unforgettably awesome battles, conquer your enemies and seize victory! Still looking for a bigger challenge? Take the next step and compete in tournaments to rise through the ranks to the top of the ratings. Think you’re tough enough? Then sharpen your tactics and tackle dynamic PvP battles from across the globe. Forget about castles and clans - jump into epic combat, take command of powerful vehicles, hone your strategic skills and become the ultimate commander. Lucky for you, Toy Defense 2 has you covered. Playtime’s over, soldier! It’s time for some real fast-paced tower defense action. I was particularly enraptured by the log furniture shop, as well as the general store that was packed to the gills with wind chimes and lawn decorations, pictured below. Speaking of old-fashioned Wild West style towns, Sisters, OR fits the bill! I felt like we should be pulling up in a stagecoach instead of a modern rental car. Old-fashioned Sisters Market, Oregon: Since 1898. Learn about tubing, and other popular water activities there.Ĭontinue Reading Bend to Portland, via Route 20Įnjoyed Bend and ready to head west again to Portland? To mix things up, we used the southern route for our return trip, taking Route 20 through stunning forests, mountains, rivers, lakes, and old-fashioned Wild West towns. What I didn’t realize until doing the drive from Portland, OR to Bend is that the west of Oregon is the classic lush greenery that I associate with Pacific Northwest destinations like nearby Seattle, Washington - but the eastern half is desert! The town of Bend sits in the middle of those opposing forces (though more in the leafy green side), and this drive takes you through each.Ī glorious feature of Bend is the river that runs through it, plus the park that embraces it. Barber Veterans Memorial Bridge in Culver, Oregon. As you stroll the area, you may notice something… Rex T. You can spend just a few minutes at the Ogden Viewpoint (it’s convenient that it’s right off the highway), or take much longer to walk the paths along the bridges. Cliff caution sign by Crooked River High Bridge. I was reminded of the danger signs at the Newport, RI Cliff Walk: The stick figures hurtling off the edge look comical, but it’s no laughing matter in reality. A 300-foot drop into the gorge of Crooked River near the bridge would be… awful. Just make sure to take the cliff warning sign pictured below seriously. Barber Veterans Memorial Bridge will take your breath away! Awe-inspiring Crooked River High Bridge near Culver, OR. At that point, don’t miss the Peter Skene Ogden State Scenic Viewpoint right along the drive through Culver, Oregon: the overlook onto Crooked River High Bridge and the Rex T. Route 97 and Culver, Oregonįurther along the northern journey from Portland to Bend, you’ll turn from your eastward Route 26 path onto Route 97 heading south. As a child of the northeast (Boston-raised, with petite Mount Greylock being the tallest hill around), imagine my ecstasy at first glimpsing towering, snow-capped Mount Hood as it peeked around the bend of Route 26! Luckily, there are several scenic overlooks with safe shoulders to pull over on, and I took full advantage of that to snap the photo below. Come take a tour of the two routes! Portland, Oregon, seen from Pittock Mansion. What was revealed is that the highways that stretch from Portland to Bend Oregon, are every bit as fabulous as the destinations, themselves. Through a series of odd (yet delightful) opportunities, I was able to do a whirlwind tour of the city before driving out to Bend, OR on Route 26 - then back to Portland via Route 20. I’d longed to visit Portland, Oregon for years, hearing rave reviews of its hipness and natural beauty. And if you're looking for even more thoughts on nature, be sure to check out our Nature Quotes list where you can snag some lines from famous nature-lovers like John Muir and Robert Frost.Share on Facebook Share on X (Twitter) Share on Pinterest Share on Email Share on WhatsApp Share on LinkedIn We've got everything from funny outdoor sayings to deeper more reflective thoughts to share with your followers. So for all of you hikers lacing up your boots, swimmers strapping on your goggles, or campers looking for the best gear for your campsite or RV, we've got a list of the perfect captions for all of the epic photos you'll be taking on your adventures in Mother Nature. Even just looking at nature photos can inspire a sense of peace to the viewer, reducing anxiety. But whether or not you would consider yourself an "outside person," we can all agree that there is a unique type of beauty and rejuvenation that comes from time spent in the great outdoors. After an extended winter and too many days forced inside by bad weather, many of us have our noses pressed against the window glass just itching to get outside. But it also provides the military and first responders with a 60% discount. Here is a clear table to see which is more customer-friendly.įrom the above chart, it indicates that Tidal HiFi Plus is much more pricey than Amazon Music Unlimited since Tidal provides higher music quality such as lossless MQA and 3D-effect Sony 360 Reality Audio. But their subscription prices are different for different detailed plans. Both of them give subscribers a 30-day free trial and a 50% discount for students. When you talk about Amazon Music HD vs Tidal HiFi price plans, the stand-out aspect about both these streaming platforms is the generosity to offer discounts for students, first responders, and military members.
Many a modern day diesel driver has experience of a truck in reduced engine power, limp mode or not starting because of issues with the emissions systems on their truck.Ī custom tune will allow the DPF filter to be removed, and turn off the EGR and SCR systems, allowing them to be removed and bringing back reliability to your truck.ĭiesel and performance enthusiasts will grin with the power gains possible through tuning, and appreciate the ability of a skilled tuner writer to properly configure other aftermarket modifications like bigger turbos, injectors, built transmissions, higher capacity fuel pumps, cold air intakes and exhausts. The DPF, EGR, and SCR systems on your 2007+ truck are complex, prone to depreciating and loosing efficiency, or outright failing and costing money to replace. Our Performance Tuners are effective for efficient DPF deletes. Transmission tuning, where applicable, is recommended to increase the transmission’s ability to handle more power by increasing line pressure and moving shift points. By having selectable tuning, you can maximize your fuel efficiency or power where needed or for fun. DELETE TUNES - 30HP - 60HP - 100HP - 150HP - 200HP - Whistle Idle - Rumble Idle 12 Valve & Lope. The modified RAM 1500 with the Cummins 6.7 engine is rated at 150 horsepower and 350 pound-feet of torque, which is enough for 2013-2018 6. 10-/3500 6.7L Note: Dodge 2013+ tuning must have unlock cable. Shop Online 0 2007.5-2021 Dodge Ram MM3 With OFFROAD EGR DPF & DEF Custom Tunes EGR & DPF Delete Kits Available MM3 Tuner with Custom Tunes for 2007 - 2021 Dodge Cummins Choose Between Power Levels Via Touch of the Button. Fits a variety of different vehicle makes. VIN Specific tune made on the dyno, custom tailored to your Cummins model Compatible with Ram 2500, 3500, 4500 & 5500. Custom DPF Delete Tune Unlock Cable & Switch for Shifting Between Power Levels Delete Tune Details. For example, a tow tune will provide a wider torque curve to assist with a heavy load. The Bully Dog Delete Tuner comes pre-loaded with DPF delete/removed tuning. Best Selling Dodge DPF & EGR Delete Tuner. Multistage custom tuning allows you to select the best power level for your application. Custom tuning can also be modified for performance modifications such as larger turbos. With custom tuning you have the option to select a power level or leave the power level stock with emissions removed. These tune files are custom written for your truck allowing safe and efficient power. Depending on your truck's model, the tune increases up to 150 horsepower and 350 pound-feet of torque. These tunes will turn off and allow the EGR and DPF emission systems to be removed. The modified RAM 1500 with the Cummins 6.7 engine is rated at 150 horsepower and 350 pound-feet of torque, which is enough for 2013-2018 6.7 Cummins Ram 2500/3500 trucks. Switch on the fly switch can be found here. This requires a Windows computer to use the HP software. If you need a device please find the bundle here. However, I’d recommend using something descriptive, like bitbucket_id_rsa so you know what it’s for later and to avoid accidentally overwriting the key if you create one for BitBucket, one for GitHub, one for your web server and so on. The private key stays on your computer and the public key is uploaded onto the server.īitBucket recommend you keep the default key name unless you have a reason to change it. The key without the extension is the private key and the key with the. Or you can list all the SSH keys you have by running: ls ~/.ssh You’ll end up with two SSH keys, one private and one public, which you can see by running: ssh-add -l set up a SSH key for BitBucket on macOS (steps 1–2 for Git).If you don’t already have a SSH key for BitBucket and/or GitHub on the particular device you’re using, you’ll need to create one for each service that you use and on each device that you will use to access your repos: If you have a SSH key already for the computer/device you’re using, you’re all set. It seems that the set-url command is applied to both fetch and push when changing the protocol, but when keeping the (SSH) protocol the same, it only updates fetch. It happened for me when I got the could not resolve hostname error above and ran set-url again. I don’t know why it works for some cases but not other ones. You don’t need to do anything further for pull because it does what fetch does (because pull is equivalent to fetch then merge). You’ll need to do the push separately by using the -push option: git remote set-url -push origin :username/reponame.git Or like this: origin :username/reponame.git (fetch) If the fetch URL has changed but the push URL has not, like this: origin :username/reponame.git (fetch) You may find that only fetch has changed - if so, the next section should help. Run git remote -v again and check the output. If it is, run set-url again, making sure to exclude the ssh:// part of the URL. Origin ssh:// :username/reponame.git (push) See if the SSH URL is prefixed with ssh://, like this: origin ssh:// :username/reponame.git (fetch) If you do, check the output from git remote -v carefully. Please make sure you have the correct access rights You might get this error: ssh: Could not resolve hostname :username: nodename nor servname provided, or not knownįatal: Could not read from remote repository. Origin :username/reponame.git (push) Troubleshooting Error: Could not resolve hostname This time, you’ll see something like this: origin :username/reponame.git (fetch) Then check what’s there again: git remote -v Type the following for BitBucket: git remote set-url origin :username/reponame.gitįor GitHub, replace with. You can see that the URLs include the protocol. This example shows a repo on BitBucket GitHub is similar. You should see a pair of entries for each remote repo (I once had origin and origin2, but that’s another story): one for fetch, which includes pull, and one for push: origin /username/reponame.git (fetch) Then check to see what you have on your server already: git remote -v Open Terminal or your command-line app of choice and navigate to your repo’s directory: cd ~/projects/reponame This is how you tell your Git server how you want to access it. This rigmarole needs to be done on each computer you intend to access your Git repo with for each repo you have that you want to access by SSH rather than by HTTPS. Here, I outline how to do it on Mac OS X, partly to remind myself how to do it in the future, partly to collate all the infomation on the internet about it and partly in the hope that someone else might find it useful. I seemed to spend a crazy amount of time trying to work out how to change access to a Git repository (repo) from HTTPS to SSH to avoid password prompts when pushing changes to BitBucket and GitHub. Add the private SSH key to your keychain.Add the public SSH key to your remote Git server. Sell it online-many websites buy and sell gift cards. You can use several methods to turn your used gift card into cash either in person or online: Turn an Apple Gift Card Into Cash OnlineĮxchange Your Apple Gift Card for Cash in Person How To Turn Your Apple Gift Card Into Cash Upload some photos of your gift card and enter your email addressĭoNotPay can even help you get some free gift cards or check the balance on many other popular brand cards, such as:.Click on the Check Gift Card Balance product.Enter your gift card number, and the page should display your balance straight awayĬheck How Much Cash Your Apple Gift Card Has Using DoNotPayĪre Apple’s methods for checking your gift card balance too slow? Why not use DoNotPay to check your Apple gift card balance in a minute? All you need to do is:.Sign in with your Apple ID and password.Check Your Balance via the WebsiteĪpple has a dedicated page for gift card balance checking that you can use the following way: You’ll get a reply via email within 48 hours. Enter your details and explain that you want to check the balance.If you prefer sending an email message to the support service, you can do so by following the instructions: You’ll have to wait about two minutes for an Apple representative to reply. Scroll to the bottom of the page and click on Chat. You can contact Apple via online chat and ask about your gift card balance. Say “gift cards” when asked about your issue, and a customer service representative will tell you your card balance. If you have a question regarding an Apple gift card, you can call the customer support line at 1-80. Using DoNotPay’s Check Gift Card Balance feature.Contacting Apple customer support by phone.If you need to check whether you have any cash left on your Apple gift card, you can do it by: Most people forget about their gift card after the first use, and it’s hard to guess the remaining balance. How To Check the Remaining Apple Gift Card Balance These cards can be reloaded and used multiple times. The way Apple gift cards work is simple-you need to activate the gift card with a 16-digit code on the back of the card using your device and then use the balance for shopping. Their gift cards can get you any software or products available in Apple web and retail stores: They all issue gift cards and won’t normally exchange them for cash unless required by law, and Apple is no different. What if we told you that you can turn an Apple gift card into cash and use it as you please?ĭoNotPay has the tools for checking any gift card balance, and if there’s money left on the card, we can send a formal request to the company demanding your money back! What Can You Do With an Apple Gift Card?Įvery company wants you to spend money in their stores, whether it’s Apple, Xbox, or Dell. Apple gift cards can get you anything from the wide range of Apple products, yet they can’t pay your bills or a nice meal. Gift cards aren’t bad, but they can’t compete with hard cash. I The Easiest Way to Convert Your Apple Gift Card to Cash Quickly
Also, as Rob's pregnant wife Jan and Beck's wife Peach, Keira Knightley and Robin Wright are both emotionally vivid and excel in thankless roles that mostly require them to act worried and wait by the phone. On the other hand, Emily Watson does a lot with a little, relaying heartbreaking emotion as Helen Wilton, the base camp's mother hen. Likewise, Jake Gyllenhaal doesn't get a lot to play, either, usually seen laying about and drinking as cocky, laid-back American dude Scott Fischer. As mailman Doug Hansen, who's driven by wanting to prove to his children that they, too, can achieve their dreams, character actor John Hawkes brings his usual Everyman quality, but he doesn't get a whole lot else to do. Introducing himself as "100% Texas," Josh Brolin's gung-ho Beck Weathers might come the closest to having a personality. Receiving top billing, Jason Clarke might be the most affecting as selfless leader Rob Hall, who already calls his unborn child "Sarah" and promises his wife that he will return back home. Nothing against any of the performances, but each character is only identified with a defining trait or a one-line backstory. The gigantic cast portraying real people is an excellent roster of talent to have attached to a film, and all of them push themselves, looking frozen to the bone. Touching the top, they all begin their way down as a brutal snowstorm blows their way, freezes their oxygen tanks, and strands the teams in "The Death Zone." Among the climbers are filthy-rich Texan doctor Beck Weathers (Josh Brolin), who's climbing against the wishes of his wife Peach (Robin Wright) divorced postal worker Doug Hansen (John Hawkes) and Japanese woman Yasuko Namba (Naoko Mori), who hopes to be the first woman to climb all "Seven Summits." After landing in Nepal and making preliminary runs before their attempt to reach the summit, thirty-four climbers spread over into three groups and make their ascent. The film follows New Zealander Rob Hall (Jason Clarke), the leader of the Adventure Consultants group's expedition, as he leaves pregnant wife Jan (Kiera Knightley) at home to go train his clients and climb the planet's highest mountain on May 10, 1996. "Everest" sluggishly takes its time getting to the summit of Mount Everest, but doesn't even take full advantage of that uphill climb in letting the viewer get a true sense of who any of these flimsily drawn people are or why they do what they do. He drops Tier 1 Helms for all classes, Obsidian Edged Blade (which is probably the item with highest sell price he drops – almost 13 gold), Bindings of the Windseeker (this one is one of the pieces needed to create Thunderfury Blessed Blade of the Windseeker, which has a selling price of almost 26 gold), Aurastone Hammer, Lava Core and much more. He guards one of the runes required to summon Ragnaros too. He is joined by 8 Firesworns Elite (level 60). This boss drops Tier 1 Gloves and Boots for most classes, of course, Essence of Fire (because he is made of fire and blood), Hand of Gehennas (which you will need for a quest), Heavy Dark Iron Ring, Crimson Shocker (wand), Ring of Spell Power (this one has a selling price of 9 gold) and other items.Ĥ. Like Magmadar, Gehenna guards one of the runes required to summon Ragnaros. It is called "Gehenna's Curse" (reduces healing effects on the target by 75% for 5 minutes), so make sure there is someone to remove it as soon as possible. Like all the other bosses, Gehennas has a signature ability as well. He is joined by two Flamewalkers Elite (level 62). The third boss at MC – Gehennas (and the second of four reptile bosses). Magmadar spits out "globs" of fire at random people throughout the fight so you will definitely need to be extra careful.ģ. He guards one of the runes required to summon Ragnaros. Also, this cute pet drops some good stuff, here are some of them: Tier 1 Pants for all classes, Core Leather, Plans: Elemental Sharpening Stone, Talisman of Ephemeral Power, Eskhandar's Right Claw, Quick Strike Ring, a bunch of weapons like Obsidian Edged Blade and Striker's Mark. But of course! How could you possibly skip petting a two-headed dog with a horn on each head and lava pouring out of each mouth?! Just adorable! "Panic"(panics nearby enemies for 8 seconds) and "Frenzy"(increases attack speed by 150 %) are the two signature abilities of this boss. As we already mentioned, Magmadar is the second boss at the Molten Core raid. Other cool drops from Lucifron are Arcanist Boots for Mage, Cenarion Boots for Druid, Choker of Enlightenment, Earthfury Boots for Shaman, Felheart Gloves for Warlock, Heavy Dark Iron Ring, Lawbringer Boots for Paladin, Essence of Fire, Ring Of Spell Power and many more.Ģ. Lucifron drops Tome of Tranquilizing shot for Hunters, which is required to defeat the second boss of Molten Core – Magmadar. This fight is all about decursing when it comes to Druids, and all about healing when it comes to Priests. As a part of a strategy, you can use two tanks – one of them will take Lucifron, and the other will take care of the Flamewalker Protector, so the main tank would avoid Cleave (which inflicts weapon damage plus 30 to an enemy and its nearest allies, affecting up to 3 targets). They have two different abilities: Cleave and Dominate mind. The icon is purple, and it has some skulls on it. This cost increase applies to all spells and abilities, whether they cost mana, rage, or energy. The cast time is instant, and it curses nearby enemies, increasing the costs of their spells and abilities by 100% for 5 minutes. His signature ability is called Lucifron's Curse. The first one you need to get rid of is Lucifron. WoW Classic Molten Core Guide - The Ten Bosses You Have To Manage With:ġ. It is time to meet that handsome dude you see every time you click on World of Warcraft Classic on your Blizzard app.Īt the same time, if you wish quick results, just get your Molten Core Carry Service from Boosting Ground! Put your diaper on before you go there because even the music will creep you out. The location we are talking about is called Blackrock Mountains, which is between Burning Steppers and The Searing Gorge, and it is pretty much linking those two regions. The Molten Core (MC) is a level 60 raid, located in the home of Ragnaros (Firelord) – the final boss of the raid. |
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